Meddeb Nihel, Amira Chiraz, Elleuch Mohamed, Cheour Elhem, Sahli Hela, Hamza Sami, Houman Habib, Miled Mohamed, Ben Chaabane Taoufik, Sellami Slaheddine
Service de Rhumatologie, Hôpital la Rabta, Tunis.
Tunis Med. 2003 Apr;81(4):245-9.
Adult onset Still's disease is a rare systemic disorder of unknown etiology occuring in young adults. The diagnosis is difficult and based upon Yamaguchi's criteria after exclusion of infectious diseases, hemotologic process or autoimmune diseases. Clinical manifestations are various. Functional prognosis depends essentially on articular involvement. We report a retrospective and multicenter study of 26 cases of adult still's disease collected during 10 years. Arthralgia are constant and arthritis are observed in third of the cases. Radiologic joint alterations are found in five cases. A literature review was done with emphasis on clinical and radiological characteristics of articular manifestations.
成人斯蒂尔病是一种病因不明的罕见系统性疾病,发生于年轻人。诊断困难,需在排除传染病、血液系统疾病或自身免疫性疾病后依据山口标准进行。临床表现多样。功能预后主要取决于关节受累情况。我们报告了一项为期10年收集的26例成人斯蒂尔病的回顾性多中心研究。关节痛持续存在,三分之一的病例出现关节炎。5例发现有放射学关节改变。我们进行了文献综述,重点关注关节表现的临床和放射学特征。