Correa-Rivas Maria S, Ferrá Ochoa Susana
Department of Pathology and Laboratory Medicine, Medical Sciences Campus, University of Puerto Rico, San Juan, Puerto Rico, PO Box 365067, San Juan, Puerto Rico 00936-5067.
P R Health Sci J. 2003 Jun;22(2):187-90.
Pulmonary sequestration is a rare developmental anomaly of the lung characterized by nonfunctional pulmonary tissue without communication with the tracheobronchial tree and receiving an aberrant systemic arterial blood supply. Few cases of non-immune hydrops fetalis associated with this entity have been reported. A 2 day old male baby born by cesarean section at 31 weeks gestational age due to fetal hydrops is presented. Autopsy revealed a hydropic baby with extralobar pulmonary sequestration and bilateral pulmonary hypoplasia. The clinicopathologic presentation of this unusual pulmonary developmental anomaly is discussed.
肺隔离症是一种罕见的肺部发育异常，其特征为无功能的肺组织，不与气管支气管树相通，并接受异常的体循环动脉血供应。与该病症相关的非免疫性胎儿水肿病例鲜有报道。本文报告了一名31周胎龄因胎儿水肿行剖宫产出生的2日龄男婴。尸检显示该水肿婴儿患有肺叶外型肺隔离症和双侧肺发育不全。本文讨论了这种不寻常的肺部发育异常的临床病理表现。
