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阻塞性孤立性支气管非霍奇金淋巴瘤——原发性结外疾病的一种罕见表现。

Obstructive solitary bronchial non-Hodgkin's lymphoma--a rare presentation of primary extranodal disease.

作者信息

Berkman N, Lafair J, Okon E, Polliack A

机构信息

Institute of Pulmonology, Hadassah University Hospital, Jerusalem, Israel.

出版信息

Leuk Lymphoma. 1992 Nov;8(4-5):405-7. doi: 10.3109/10428199209051021.

DOI:10.3109/10428199209051021
PMID:1290965
Abstract

Endobronchial involvement by non-Hodgkin's lymphoma (NHL) is uncommon and usually occurs in the presence of more generalised disease. Solitary endobronchial lymphoma in the absence of disease elsewhere is extremely rare. In this report we describe a patient with an obstructing endobronchial mass which was the initial manifestation of NHL. The patient was treated initially with radiotherapy followed by cyclic combination chemotherapy with initial complete resolution of the endobronchial disease. However, he subsequently developed widespread lymphoma. This unusual presentation of NHL is discussed and the relevant literature is reviewed.

摘要

非霍奇金淋巴瘤(NHL)累及支气管内的情况并不常见,通常发生于存在更广泛病变时。在无其他部位病变的情况下,孤立性支气管内淋巴瘤极为罕见。在本报告中,我们描述了一名患者,其支气管内有阻塞性肿块,这是NHL的初始表现。该患者最初接受了放射治疗,随后进行了周期性联合化疗,支气管内病变最初完全消退。然而,他随后发展为广泛的淋巴瘤。本文讨论了NHL这种不寻常的表现形式,并对相关文献进行了综述。

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