Massin M, Leroy P, Misson J P, Lepage P
Département universitaire de pédiatrie, CHR citadelle, université de Liège, 1, boulevard du 12e-de-Ligne, 4000 Liège, Belgique.
Arch Pediatr. 2003 Jun;10(6):524-6. doi: 10.1016/s0929-693x(03)00150-7.
Catecholaminergic polymorphic ventricular tachycardia is important to be diagnosed as an underlying disease in children with syncope and normal heart, because of its poor prognosis.
A 3-year-old boy was referred for stress and emotion induced syncope. Primary ventricular arrhythmia, consisting of salvos of bidirectional ventricular tachycardia, was reproducibly induced by physical exertion. The syncopal events and severe arrhythmia disappeared with beta-blocking therapy.
Despite its rare occurrence, catecholaminergic polymorphic ventricular tachycardia is an important cause of stress and emotion induced syncope and sudden death in children.
由于儿茶酚胺能多形性室性心动过速预后较差，因此对于晕厥且心脏正常的儿童，将其诊断为潜在疾病很重要。
一名3岁男孩因应激和情绪诱发的晕厥前来就诊。体力活动可重复性诱发由成对双向室性心动过速组成的原发性室性心律失常。β受体阻滞剂治疗后，晕厥事件和严重心律失常消失。
尽管儿茶酚胺能多形性室性心动过速发生率较低，但它是儿童应激和情绪诱发晕厥及猝死的重要原因。
