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克雅氏病中的全面性惊厥性癫痫持续状态

Generalized convulsive status epilepticus in Creutzfeldt-Jakob disease.

作者信息

Neufeld Miri Y, Talianski-Aronov Alisia, Soffer Dov, Korczyn Amos D

机构信息

Department of Neurology, EEG and Epilepsy Unit, Tel-Aviv Sourasky Medical Center, Tel-Aviv 64239, Israel.

出版信息

Seizure. 2003 Sep;12(6):403-5. doi: 10.1016/s1059-1311(02)00378-3.

DOI:10.1016/s1059-1311(02)00378-3
PMID:12915087
Abstract

We report a patient who was referred to our department because of generalized status epilepticus. His condition deteriorated rapidly and he died 1 month after admission. Autopsy confirmed the clinical diagnosis of Creutzfeldt-Jakob disease (CJD). CJD should be added to the list of rare but possible causes of generalized status epilepticus.

摘要

我们报告了一名因全身性癫痫持续状态转诊至我科的患者。他的病情迅速恶化,入院1个月后死亡。尸检证实了克雅氏病(CJD)的临床诊断。CJD应被列入全身性癫痫持续状态罕见但可能的病因清单中。

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引用本文的文献

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Cureus. 2022 Aug 31;14(8):e28649. doi: 10.7759/cureus.28649. eCollection 2022 Aug.
2
Creutzfeldt-Jakob disease with Alzheimer pathology, presenting with status epilepticus following repeated partial seizures: a case report and literature review.伴有阿尔茨海默病病理特征的克雅氏病,反复部分性癫痫发作后出现癫痫持续状态:一例报告及文献综述
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Treating seizures in Creutzfeldt-Jakob disease.
治疗克雅氏病中的癫痫发作。
Epilepsy Behav Case Rep. 2014 Feb 7;2:75-9. doi: 10.1016/j.ebcr.2014.01.004. eCollection 2014.
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Unraveling the neuroprotective mechanisms of PrP (C) in excitotoxicity.解析 PrP(C)在兴奋毒性中的神经保护机制。
Prion. 2012 Jul 1;6(3):245-51. doi: 10.4161/pri.19639.