Stocker M, Gessler P, Wolf R, Bänzinger O
Department of Pediatric Intensive Care, University Childrens Hospital, Zürich, Switzerland.
Klin Padiatr. 2003 Jul-Aug;215(4):205-7. doi: 10.1055/s-2003-41396.
At the age of 5 years, a boy with known multicystic dysplastic kidney disease showed signs of arterial hypertension with progress to fatal hypertensive encephalopathy. Arterial hypertension was refractory to antihypertensive therapy and the child lost consciousness. Computed tomography of the brain revealed multiple cerebral infarctions. Doppler ultrasound showed an elevation of blood flow in the main artery of the functioning kidney consistent with stenosis as a cause of hypertension.
Arterial hypertension is a known complication of kidney disease. Multicystic dysplastic kidney and renal artery stenosis is a potentially fatal association. Careful evaluation and monitoring, with special emphasis on blood pressure, should be performed in children with multicystic dysplastic kidney disease.
一名患有多囊性发育不良肾病的5岁男孩出现动脉高血压症状，并进展为致命的高血压脑病。动脉高血压对抗高血压治疗无效，孩子失去意识。脑部计算机断层扫描显示多处脑梗死。多普勒超声显示，功能正常的肾脏主动脉血流升高，符合作为高血压病因的狭窄表现。
动脉高血压是已知的肾病并发症。多囊性发育不良肾与肾动脉狭窄是一种潜在的致命关联。对于患有多囊性发育不良肾病的儿童，应进行仔细评估和监测，尤其要关注血压。
