Zinka E, Czarnecki L
Pracowni Badań Nieinwazyjnych Układu Krazenia przy Oddziele Internistyczno-Kardiologicznym Wojewódzkiego Szpitala w Koszalinie.
Wiad Lek. 1992 Sep;45(17-18):715-8.
A case is presented of fulminant endocardial elastosis in a 5-week-old infant. The baby died after four days from the appearance of the first pathological symptoms with evidence of extreme circulatory insufficiency. Of main importance for intravital diagnosis was echocardiographic examination. The autopsy confirmed the diagnosis. The myocardium was hypertrophic without evidence of inflammation. The typical changes for this disease were found in parietal endocardium of both ventricles, both atria, as well as both atrioventricular valves, and aortic valve.
本文报告一例5周龄婴儿暴发性心内膜弹力纤维增生症。自首次出现病理症状起4天后,该婴儿死于严重循环功能不全。超声心动图检查对生前诊断至关重要。尸检证实了诊断。心肌肥厚,无炎症迹象。在左右心室、左右心房的壁层心内膜以及房室瓣和主动脉瓣均发现了该病的典型变化。