Slight R D, Nzewi O C, Sivaprakasam R, Mankad P S
Department of Cardiothoracic Surgery, The Royal Infirmary of Edinburgh, Little France, Edinburgh, UK.
Heart. 2003 Oct;89(10):e26. doi: 10.1136/heart.89.10.e26.
Cor triatriatum sinister is a rare congenital defect in which the left atrium is divided by a fibromuscular membrane into two distinct chambers. Classically, patients present in infancy although in some cases they remain asymptomatic until adulthood. The clinical features on presentation can mimic those of mitral stenosis due to the obstructive properties of the membrane. Cor triatriatum sinister presented in this case in an adult as mitral stenosis. Factors that may be relevant in determining late presentation are also discussed.
左房三房心是一种罕见的先天性缺陷，其中左心房被纤维肌性隔膜分隔为两个不同的腔室。典型情况下，患者在婴儿期发病，不过在某些病例中，他们直到成年都无症状。由于隔膜的阻塞特性，发病时的临床特征可类似于二尖瓣狭窄。该病例中的左房三房心在一名成年人中表现为二尖瓣狭窄。文中还讨论了可能与延迟发病相关的因素。
