Kovanlikaya A, Pirnar T, Olgun N
Department of Radiology, Dokuz Eylul University, Izmir, Turkey.
Pediatr Radiol. 1992;22(2):155. doi: 10.1007/BF02011326.
A case of pulmonary blastoma is presented with review of the radiographic, ultrasonographic and CT appearances of this rare malignant tumor of children. Pulmonary blastoma arises from primitive lung mesenchyma and histologically resembles fetal lung. The clinical presentation is usually respiratory distress. The prognosis of the disease is poor even if surgical resection, supplemental chemotherapy and radiation therapy are performed. We present a case of pulmonary blastoma who died two days after surgical resection.
本文报告一例肺母细胞瘤病例,并回顾了这种罕见儿童恶性肿瘤的放射学、超声及CT表现。肺母细胞瘤起源于原始肺间充质,组织学上类似胎儿肺。临床表现通常为呼吸窘迫。即使进行手术切除、辅助化疗和放疗,该病的预后也很差。我们报告一例肺母细胞瘤患者,其在手术切除后两天死亡。