Giron J, Eynius F, Joffre P, Senac J P, Marty-Ané C, Mary H, Baldet P
Service de Radiologie, Hôpital St-Charles, Montpellier.
J Radiol. 1989 Dec;70(12):725-9.
A case of pneumoblastoma concerning a 33 year old man, incidentally discovered on a systematic chest X Ray, is reported. The radiologic findings include a voluminous and peripherical mass with necrotic zones. The pathologic findings in optic microscopy and the special technics consist in the three cellular contingents which form the pneumoblastoma: clusters of indifferentiated cells, epithelial cells and spindle cells. All the features show clearly a blastomatic character very similar to a foetal lung which allows to differentiate the pulmonary blastoma from carcinosarcoma. The authors, through a review of the literature, demonstrate the rarity (less than 100 cases reported), the malignant evolution which metastasis and the age (strong majority of adults) which characterize this pathology.
报告了一例33岁男性的肺母细胞瘤病例，该病例在系统性胸部X光检查中偶然发现。放射学检查结果包括一个体积较大的外周肿块，伴有坏死区域。光学显微镜和特殊技术下的病理检查结果显示，肺母细胞瘤由三种细胞成分组成：未分化细胞簇、上皮细胞和梭形细胞。所有特征均清晰显示出与胎儿肺非常相似的母细胞特征，这有助于将肺母细胞瘤与癌肉瘤区分开来。作者通过文献回顾，证明了这种病理特征的罕见性（报道病例少于100例）、具有转移特性的恶性进展以及发病年龄（绝大多数为成年人）。
