Delmas M C, Cochat P, Ranchin B, Négrier C, Barre P, Bouvier R, David L
Unité de néphrologie pédiatrique, hôpital E Herriot, Lyon, France.
Pediatrie. 1992;47(1):31-5.
The authors report on the case of a child with the nephrotic syndrome complicated by thrombosis of superior longitudinal sinus, bilateral massive pulmonary embolism resulting in a sudden death. A dramatic deficiency in factor XII was demonstrated; the pathophysiology and management of such an abnormality are discussed.