Charachon R, Gratacap B, Fillatre B
C.H.U. de Grenoble, Clinique Universitaire O.R.L., France.
Rev Laryngol Otol Rhinol (Bord). 1992;113(1):7-10.
In a series of 16 middle ear cholesteatomas of a congenital type are reported in children; the youngest (18 months) presented with a bilateral case. Whereas a simple tympanoplasty could cure a localized pearl, typically anterosuperior in the mesotympanum, the stapes is fast eroded (7 cases) if progression goes on. Intact canal wall technique in 2 stages was the typical procedure. Good hearing results were generally achieved (except in one case of fixed footplate): 9 cases/14 with an ABG within 20 dB and an AC level within 30 dB.
本文报告了一系列16例儿童先天性中耳胆脂瘤；最年幼者（18个月）为双侧病例。对于位于中鼓室典型的前上方的局限性胆脂瘤，单纯鼓室成形术可治愈，但如果病情进展，镫骨会很快被侵蚀（7例）。两期完整外耳道壁技术是典型的手术方法。一般能取得良好的听力结果（除1例镫骨足板固定外）：14例中有9例气骨导差在20dB以内，气导水平在30dB以内。
