Robinson D, Hambleton G
Arch Dis Child. 1977 Feb;52(2):155-7. doi: 10.1136/adc.52.2.155.
A 3-month-old infant presented with multiple cutaneous haemangiomata, and was found to have a cardiac murmur and hepatomegaly. The latter increased strikingly over the next 3 months, and was accompanied by cardiomegaly. Other usual signs of congestive cardiac failure were not present, however, and an arteriogram showed the presence of a grossly abnormal vascular pattern in the liver, confirming the clinical suspecions of hepatic haemangiomatosis. Two short courses of steroid therapy resulted in a marked but temporary decrease in liver size. After the age of one year, however, there was gradual regression of all abnormal clinical signs without further therapy.
一名3个月大的婴儿出现多处皮肤血管瘤,同时发现有心脏杂音和肝肿大。在接下来的3个月里,肝肿大显著加重,并伴有心脏扩大。然而,并未出现其他常见的充血性心力衰竭体征,血管造影显示肝脏存在明显异常的血管形态,证实了临床对肝血管瘤病的怀疑。两个短疗程的类固醇治疗使肝脏大小显著但暂时缩小。然而,1岁以后,所有异常临床体征在未进一步治疗的情况下逐渐消退。