Rosenbusch G, Hoefinagels W H, Koene R A, Penn W, Thijssen H O
Rofo. 1977 Mar;126(3):218-27. doi: 10.1055/s-0029-1230568.
Vascular involvement in von Recklinghausen's neurofibromatosis has been known since the work of Reubi (1944, 1946). We found 72 cases of neurofibromatosis with renovascular hypertension reported in the literature. We have observed three female patients, of whom two had unilateral renal artery abnormalities consisting of stensoses and small aneurysms. The third patient, who had a right-sided nephrectomy for probable occlusion of the renal artery, had a coarctation of the abdominal aorta and complete occlusion of the left renal artery and of the coeliac-mesenteric trunk. There were, in addition, large, bilateral aneurysms in the circle of Willis.
自鲁比(1944年、1946年)开展研究以来,人们便知晓冯·雷克林霍增氏神经纤维瘤病会累及血管。我们在文献中发现了72例伴有肾血管性高血压的神经纤维瘤病病例。我们观察了三名女性患者,其中两名患者存在单侧肾动脉异常,包括狭窄和小动脉瘤。第三名患者因可能的肾动脉闭塞接受了右侧肾切除术,其腹主动脉缩窄,左肾动脉及腹腔 - 肠系膜干完全闭塞。此外,在Willis环处还有双侧大动脉瘤。