ASAY L D
Calif Med. 1965 Apr;102(4):292-300.
Cystic fibrosis, a disease thought to be transmitted as a recessive genetic trait, is found as a disease in about one in 1,000 to one in 10,000 births. It involves all of the exocrine glands with presenting symptoms dependent upon the extent of involvement of any group of glands. Many aspects of the disease can be corrected by substitution therapy. This applies particularly to the use of animal pancreas for the steatorrhea and salt for prevention of heat prostration. Unfortunately, the obstructive pulmonary disease with secondary bronchial infections can only be treated symptomatically by the use of mucus thinning agents, postural drainage, and antibiotics. Nevertheless, longevity can be increased and a great deal of hope offered to the families of these unfortunate children by careful supervision of their medical care.
囊性纤维化是一种被认为以隐性遗传特征传播的疾病，在大约每1000至10000例出生中就有1例出现。它累及所有外分泌腺，出现的症状取决于任何一组腺体的受累程度。该疾病的许多方面可以通过替代疗法得到纠正。这尤其适用于使用动物胰腺治疗脂肪泻以及使用盐分预防中暑。不幸的是，伴有继发性支气管感染的阻塞性肺部疾病只能通过使用黏液稀释剂、体位引流和抗生素进行对症治疗。尽管如此，通过对这些不幸儿童的医疗护理进行仔细监督，可以延长他们的寿命，并给他们的家庭带来很大希望。
