Lupo I, Ciulla L, Cusimano F, Fierro B, Piccoli F
Institute of Neuropsychiatry, University of Palermo, Italy.
Acta Neurol (Napoli). 1992 Jun;14(3):163-72.
Brainstem auditory evoked potentials (BAEPs) were evaluated in three patients with mitochondrial encephalomyopathy belonging to the same family. This study showed marked alterations of BAEPs in all patients: reduction of wave amplitude, poor repeatability of responses in test-retest and abnormalities in wave form and latency. The neuroradiological examinations (CT-scan, MRI) did not show significant structural brain abnormalities. Abnormal BAEPs in our patients may be related to central metabolic disorder rather than hearing loss.