Hurley Maja E, O'Meara Anne, Fogarty Esmond, Hayes Roisin
Department of Radiology, Our Lady's Hospital for Sick Children, Crumlin, Dublin 12, Ireland.
Pediatr Radiol. 2004 Mar;34(3):267-70. doi: 10.1007/s00247-003-1065-8. Epub 2003 Oct 15.
This report describes a 5-year-old girl with Langerhans' cell histiocytosis (LCH) of the clivus. To date only five patients, including our patient, have been described with LCH at this site. Our patient differs from those previously reported by her atypical clinical presentation with torticollis, but without a sixth nerve palsy. In addition, she is the first patient to present with concomitant disease elsewhere at the time of diagnosis, i.e. both femoral necks and left proximal humerus. Our patient thus presents unique features and underlines the importance of including LCH in the differential diagnosis of erosive lesions of the clivus.
本报告描述了一名患有斜坡朗格汉斯细胞组织细胞增多症（LCH）的5岁女孩。迄今为止，包括我们的患者在内，仅有5例患者被报道在该部位患有LCH。我们的患者与之前报道的患者不同，其临床表现为非典型斜颈，但无第六神经麻痹。此外，她是首例在诊断时伴有其他部位疾病的患者，即双侧股骨颈和左肱骨近端。因此，我们的患者具有独特的特征，并强调了在斜坡侵蚀性病变的鉴别诊断中纳入LCH的重要性。
