Khoda J, Sebbag G, Lantzberg L, Levi Y, Gavriel A, Barki Y, Hertzanu Y
Service de Chirurgie A Générale et Vasculaire, Centre Hospitalo-Universitaire Soroka Ecole des Sciences Médicales, Université Ben Gourion du Neguev, Beer Sheva, Israël.
Ann Chir. 1992;46(7):636-41.
We present our experience of 10 cases of pseudomyxoma peritonei treated in our regional hospital between 1978 and 1992. We note the rarity of this disease; the catastrophic macroscopic appearance may mislead the in experienced surgeon. Preoperative diagnosis is usually easy when confronted with a mass in an ascitic abdomen, with the help of ultrasonography and CT-scan, and above all after abdominal puncture which produces pathognomonic gelatinous fluid. Most cases are derived from the ovary and appendix. Treatment is surgical and aggressive; we adopt the protocol proposed by Sugarbaker which combines repeated surgery and local and systemic chemotherapy. The relatively good survival, even in the malignant cases, seems to be improved by this treatment.
我们介绍了1978年至1992年间在我们地区医院治疗的10例腹膜假黏液瘤的经验。我们注意到这种疾病很罕见；其灾难性的大体外观可能会误导经验不足的外科医生。当面对腹水腹部的肿块时，借助超声检查和CT扫描，术前诊断通常很容易，尤其是在腹腔穿刺抽出特征性胶冻状液体之后。大多数病例起源于卵巢和阑尾。治疗是手术性的且积极；我们采用Sugarbaker提出的方案，该方案结合了重复手术以及局部和全身化疗。即使是恶性病例，这种治疗似乎也能改善相对较好的生存率。
