Germain A, Hureau J, Seddik A, Lafargue J P, Preel J L
Service de Chirurgie, hôpital de Nanterre.
Chirurgie. 1992;118(6-7):348-54; discussion 355.
Peritoneal pseudomyxoma is a rare disease (400 published cases). In 60% of all cases, an ovarian tumor is the cause of the disease. The second cause is appendicular mucocele. We report about four personal cases after a longer time lapse. No clinical or biological sign is specific. Ultrasonography associated to CT may allow establishing the preoperative diagnosis. Peritoneal pseudomyxoma has several main features: it is insidious, recurrent, obstinate and severe. Recent work has shown that peritoneal pseudomyxoma is secondary to malignant mucosecretory tumors, mainly of ovarian (cystadenocarcinoma) or appendicular origin, with intraperitoneal cell implants. Surgery is the only treatment with proven effectiveness. The effectiveness of chemotherapy and radiation therapy has not been established.
腹膜假黏液瘤是一种罕见疾病（已发表400例病例）。在所有病例中，60%的病因是卵巢肿瘤。第二大病因是阑尾黏液囊肿。我们报告4例个人病例，时间跨度较长。没有特异性的临床或生物学体征。超声检查结合CT可能有助于术前诊断。腹膜假黏液瘤有几个主要特征：隐匿性、复发性、顽固性和严重性。最近的研究表明，腹膜假黏液瘤继发于恶性黏液分泌性肿瘤，主要起源于卵巢（囊腺癌）或阑尾，并伴有腹腔内细胞种植。手术是唯一经证实有效的治疗方法。化疗和放疗的有效性尚未得到证实。
