Corbo M, Quattrini A, Lugaresi A, Santoro M, Latov N, Hays A P
Department of Neurology, College of Physicians and Surgeons, Columbia University, New York, NY 10032.
Ann Neurol. 1992 Oct;32(4):487-93. doi: 10.1002/ana.410320402.
Human anti-GM1 antibodies from patients with lower motor neuron disease or predominantly motor neuropathy recognize carbohydrate determinants shared by GM1 and related glycolipids and glycoproteins, but the identity of the antigens to which they bind in tissue is unknown. We examined the binding of anti-GM1 antibodies with differing fine specificities to spinal cord, isolated motor neurons, and dorsal root ganglia neurons in order to characterize the tissue antigens. All anti-GM1 antibodies tested bound to the surface of bovine spinal motor neurons and immunostained the gray matter of unfixed sections of spinal cord. The staining was blocked by cholera toxin, which is specific for GM1, indicating that GM1 itself was the target antigen. Binding to white matter was more variable and depended on fixation and the fine specificities of the antibodies. The anti-GM1 antibodies did not bind to dorsal root ganglia neurons in tissue sections or in culture. These studies suggest that the autoantibodies might exert their effect, in part, by binding to GM1 on the surface of motor neurons, and that the absence of binding to dorsal root ganglia neurons might explain the lack of sensory abnormalities in affected patients.
来自下运动神经元疾病或主要为运动神经病患者的人抗GM1抗体识别GM1以及相关糖脂和糖蛋白共有的碳水化合物决定簇,但它们在组织中所结合抗原的身份尚不清楚。我们检测了具有不同精细特异性的抗GM1抗体与脊髓、分离的运动神经元和背根神经节神经元的结合情况,以表征组织抗原。所有测试的抗GM1抗体均与牛脊髓运动神经元表面结合,并对脊髓未固定切片的灰质进行免疫染色。染色被对GM1特异的霍乱毒素阻断,表明GM1本身就是靶抗原。与白质的结合更具变异性,且取决于固定情况和抗体的精细特异性。抗GM1抗体在组织切片或培养物中均不与背根神经节神经元结合。这些研究表明,自身抗体可能部分通过与运动神经元表面的GM1结合发挥作用,而不与背根神经节神经元结合可能解释了受影响患者缺乏感觉异常的原因。