Tofield Christopher E, Mackinnon Craig A
Consultant Plastic and Reconstructive Surgeon, Wellington Regional Plastic, Maxillofacial and Burns Unit, Hutt Hospital, Lower Hutt, New Zealand.
Cleft Palate Craniofac J. 2003 Nov;40(6):629-31. doi: 10.1597/02-159.
Spondyloepiphyseal dysplasia congenita (SEDC) is a rare, inheritable condition that can include dwarfism, cleft palate, and C(1-2) instability. When repairing a cleft palate in a patient with SEDC, there is a significant risk of cord compression at the C(1-2) level because of neck hyperextension required for the operation. This reports presents a patient with SEDC who underwent surgery for a cleft palate, using a Ferno vacuum splint to immobilize the spine.
The patient underwent general anesthesia. Good access was gained to the palate, and it was repaired without any complications. Particular attention was paid to maintaining the neck in a neutral position.
The described technique provides the patient with the safest possible situation during anesthesia for cleft palate repair.
先天性脊椎骨骺发育不良（SEDC）是一种罕见的遗传性疾病，可包括侏儒症、腭裂和C（1-2）不稳定。在为患有SEDC的患者修复腭裂时，由于手术需要颈部过度伸展，C（1-2）水平存在脊髓受压的重大风险。本报告介绍了一名患有SEDC的患者，该患者接受了腭裂手术，使用费尔诺真空夹板固定脊柱。
患者接受全身麻醉。顺利进入腭部，修复过程无任何并发症。特别注意保持颈部处于中立位置。
所描述的技术为腭裂修复麻醉期间的患者提供了尽可能安全的状况。
