Gaona-Luviano Patricia, Unda-Franco Eduardo, González-Jara Lizbeth, Romero Penélope, Medina-Franco Heriberto
Department of Gynecology, Nacional Institute of Medical Sciences and Nutrition "Salvador Zubirán," Mexico City, Mexico.
Gynecol Oncol. 2003 Nov;91(2):456-8. doi: 10.1016/s0090-8258(03)00500-6.
Primitive neuroectodermal tumor is grouped together with Ewing sarcoma of the bone, but its presentation includes a wider age range and more central locations than its osseous counterpart. Presentation in vagina is exceedingly rare.
A 34-year-old woman with personal history of kidney transplant presented with a painless vaginal mass. After surgical excision, pathology results demonstrated a primitive neuroectodermal tumor. Chemotherapy was given, followed by external beam and vaginal intracavitary brachytherapy. After 20 months postexcision, there is no clinical nor radiographic evidence of recurrence.
This is the second case of primitive neuroectodermal tumor located in the vagina reported in the literature.
原始神经外胚层肿瘤与骨尤文肉瘤归为一类，但与骨尤文肉瘤相比，其发病年龄范围更广，发病部位更靠近中心。阴道原发性神经外胚层肿瘤极为罕见。
一名有肾移植个人史的34岁女性，出现无痛性阴道肿物。手术切除后，病理结果显示为原始神经外胚层肿瘤。给予化疗，随后进行外照射和阴道腔内近距离放疗。切除术后20个月，无临床及影像学复发证据。
这是文献报道的第二例位于阴道的原始神经外胚层肿瘤。
