Guo Zhi-fu, Yao Xiao-peng, Li Qiang, Bai Chong, Liu Zhong-ling
Department of Respiratory Diseases, Changhai Hospital, Second Military Medical University, Shanghai 200433, China.
Zhonghua Jie He He Hu Xi Za Zhi. 2003 Oct;26(10):626-9.
To describe the clinical features of pulmonary epithelioid hemangioendothelioma.
With a case report and review of the related literatures, the etiology, clinical manifestations, diagnosis, differential diagnosis, management and prognosis of pulmonary epithelioid hemangioendothelioma were described.
The etiology of this rare disease remains unknown. Symptoms are scanty and usually mild; chest radiograph or computed tomography usually reveals multiple bilateral pulmonary nodules. Primitive lumen formed by a single cell is the pathologic feature. Immunohistochemical stains show that the malignant cells are of the endothelial type. There is no effective treatment for this disease and its prognosis is unpredictable.
Pulmonary epithelioid hemangioendothelioma is rare and often misdiagnosed as other pulmonary diseases.
描述肺上皮样血管内皮瘤的临床特征。
通过病例报告并复习相关文献，对肺上皮样血管内皮瘤的病因、临床表现、诊断、鉴别诊断、治疗及预后进行描述。
这种罕见疾病的病因尚不清楚。症状较少且通常较轻；胸部X线片或计算机断层扫描通常显示双侧肺部多个结节。由单个细胞形成的原始管腔是其病理特征。免疫组织化学染色显示恶性细胞为内皮型。该病尚无有效治疗方法，其预后不可预测。
肺上皮样血管内皮瘤罕见，常被误诊为其他肺部疾病。
