Datta C K, Mossallati S, Hess D R, Brager P M, Basha I S
United Hospital Center, Clarksburg, USA.
W V Med J. 2000 Jan-Feb;96(1):364-6.
An extremely rare case of pulmonary epitheloid hemangioendothelioma (PEH), previously known as intravascular bronchoalveolar tumor (IVBAT), in a 38-year-old female is presented. This patient had a history of rheumatoid arthritis and bilateral multiple small pulmonary nodules which progressed over the years. The histopathological diagnosis of PEH was confirmed by immunohistochemical stains. Prognosis of this tumor is very unpredictable. There is no effective treatment for pulmonary epitheloid hemangioendothelioma.
本文报告了一例极为罕见的肺上皮样血管内皮瘤（PEH），该疾病既往被称为血管内支气管肺泡肿瘤（IVBAT），患者为一名38岁女性。该患者有类风湿关节炎病史，多年来双侧肺部出现多个小结节且病情进展。通过免疫组化染色确诊为肺上皮样血管内皮瘤。该肿瘤的预后非常难以预测。目前尚无针对肺上皮样血管内皮瘤的有效治疗方法。
