一名克罗恩病患者的皮肤韦格纳肉芽肿（恶性脓皮病）

Cutaneous Wegener's granulomatosis (malignant pyoderma) in a patient with Crohn's disease.

作者信息

Jacob Sharon E, Martin Lucy K, Kerdel Francisco A

机构信息

Department of Dermatology and Cutaneous Surgery, University of Miami School of Medicine, Miami, FL, USA.

出版信息

Int J Dermatol. 2003 Nov;42(11):896-8. doi: 10.1046/j.1365-4362.2003.01919.x.

DOI:10.1046/j.1365-4362.2003.01919.x

PMID:14636208

Abstract

We report a case of an unusual presentation of Wegener's granulomatosis (WG) in a patient with Crohn's disease (CD). She presented to our Wound Care Center with 7th cranial nerve palsy and facial pyoderma-like ulcerations. Although WG has a predilection for the lung, kidney, and eyes, cutaneous involvement can be seen in 50% of the cases, and it can be the presenting sign in 9-14%. Because of the lethality of WG if not properly treated, the diagnosis is imperative.

摘要

我们报告了1例克罗恩病（CD）患者出现韦格纳肉芽肿病（WG）异常表现的病例。她因第7颅神经麻痹和面部脓皮病样溃疡就诊于我们的伤口护理中心。尽管WG好发于肺、肾和眼，但50%的病例可见皮肤受累，且9%-14%的病例中皮肤受累可为首发症状。由于WG若未得到恰当治疗会有致命性，因此必须进行诊断。