Ha Chungyoon Y, Messieha Zakaria S
General Practice Residency, University of Illinois at Chicago, IL 1160612, USA.
Spec Care Dentist. 2003;23(3):111-6. doi: 10.1111/j.1754-4505.2003.tb01671.x.
Möbius syndrome is a rare congenital disorder with the primary diagnostic criteria of congenital facial and abducent nerve palsy. Orofacial anomalies and limb malformations may be associated with the disorder. Involvement of other cranial nerves also is common. Occasionally, the V, X, XI, and XII cranial nerves are involved, resulting in difficulty of chewing, swallowing, and coughing, which often leads to respiratory complications. Mental retardation and autism have been reported in some cases. An 18-year-old Hispanic male came to the General Practice Residency clinic at the University of Illinois at Chicago for dental treatment. The patient had a history of Möbius syndrome, mental retardation, and behavioral problems. Because of acute situational anxiety and violent behavior, we arranged for the patient to have general anesthesia while we provided complete oral rehabilitation. This article discusses the treatment of a patient, including special considerations taken during anesthesia and dental management. A review of the special challenges concerning patients with such a condition are reviewed.
莫比乌斯综合征是一种罕见的先天性疾病，主要诊断标准为先天性面神经和展神经麻痹。口面部异常和肢体畸形可能与该疾病相关。其他颅神经受累也很常见。偶尔，第V、X、XI和XII颅神经会受累，导致咀嚼、吞咽和咳嗽困难，这常常会引发呼吸并发症。在某些病例中还报告有智力障碍和自闭症。一名18岁的西班牙裔男性来到芝加哥伊利诺伊大学的全科医学住院诊所接受牙科治疗。该患者有莫比乌斯综合征、智力障碍和行为问题病史。由于急性情境性焦虑和暴力行为，我们安排患者在接受全身麻醉的同时进行全面的口腔修复治疗。本文讨论了该患者的治疗情况，包括麻醉和牙科管理过程中的特殊注意事项。还对这类患者所面临的特殊挑战进行了综述。
