Iwase Jinichi, Tajima Kazuyoshi, Io Akinori, Minho Song, Katou Wataru, Tanaka Keisuke
Department of Cardiovascular Surgery, Nagoya Daini Red Cross Hospital, Nagoya, Japan.
Jpn J Thorac Cardiovasc Surg. 2003 Nov;51(11):612-5. doi: 10.1007/BF02736702.
Stenotic lesion of the left coronary artery is an unnoticed but complicating feature of supravalvular aortic stenosis (SAS). We present successful repair of SAS with left coronary ostial stenosis. A 9-year-old girl was diagnosed as Williams syndrome associated with SAS. She had no symptoms of angina but cardiac catheterization revealed severe stenosis of the left coronary artery ostium. We adopted Brom's three patch technique, which could enlarge the aortic root and ostial lesion of left coronary artery inclusively. This method is also ideal regarding restoration of the aortic root geometry.
左冠状动脉狭窄病变是瓣上主动脉狭窄（SAS）一个未被注意但却复杂的特征。我们展示了对伴有左冠状动脉开口狭窄的SAS的成功修复。一名9岁女孩被诊断为与SAS相关的威廉姆斯综合征。她没有心绞痛症状，但心脏导管检查显示左冠状动脉开口严重狭窄。我们采用了布罗姆三补片技术，该技术可以整体扩大主动脉根部和左冠状动脉开口病变。就主动脉根部几何形状的恢复而言，这种方法也是理想的。
