Cardiovascular Surgery, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.
Pediatric Cardiology, Japan Community Health Care Organization, Kyushu Hospital, Fukuoka, Japan.
Multimed Man Cardiothorac Surg. 2021 Aug 20;2021. doi: 10.1510/mmcts.2021.062.
Left coronary ostial stenosis, which is associated with sudden death, occasionally occurs in individuals with Williams syndrome. However, surgical methods that provide reliable long-term revascularization remain unknown among infants and young children with coronary ostial stenosis. We describe the case of an 18-month-old boy with Williams syndrome who presented with cardiogenic shock due to left coronary ostial stenosis. We performed patch augmentation of the left coronary ostium using glutaraldehyde-treated autologous pericardium. At the last follow-up, the patient was well without any adverse events or myocardial ischemia.
左冠状动脉口狭窄，与猝死有关，偶发于威廉姆斯综合征患者。然而，婴儿和幼儿的冠状动脉口狭窄，可靠的长期血运重建方法仍不明确。我们描述了一例 18 个月大的男孩，因左冠状动脉口狭窄导致心源性休克。我们采用戊二醛处理的自体心包片对左冠状动脉口进行修补增强。末次随访时，患儿情况良好，无不良事件或心肌缺血发生。
