Lee Yung-Chin, Huang Shu-Pin, Liu Chia-Chu, Wu Wen-Jeng, Chou Yii-Her, Huang Chun-Hsiung
Department of Urology, Chung-Ho Memorial Hospital, Kaohsiung Medical University, Kaohsiung, Taiwan.
Kaohsiung J Med Sci. 2003 Nov;19(11):579-82. doi: 10.1016/S1607-551X(09)70510-8.
Extrarenal angiomyolipoma is an uncommon disease entity and is rare in the retroperitoneum. We report a case of giant extrarenal retroperitoneal angiomyolipoma mimicking liposarcoma. A 35-year-old woman presented with a history of increased abdominal circumference and urinary frequency. Abdominal computerized tomography demonstrated a 24 x 21 x 16 cm retroperitoneal fatty tumor displacing the right kidney to the left upper quadrant of the abdomen. At laparotomy, the tumor was widely excised and the right kidney was successfully preserved. Final histologic examination identified the tumor as an angiomyolipoma. At 4-month postoperative follow-up, no evidence of tumor recurrence was found and the right kidney was fully functional.
肾外血管平滑肌脂肪瘤是一种罕见的疾病实体，在腹膜后更为少见。我们报告一例巨大的肾外腹膜后血管平滑肌脂肪瘤，其表现类似脂肪肉瘤。一名35岁女性，有腹围增大和尿频病史。腹部计算机断层扫描显示一个24×21×16 cm的腹膜后脂肪性肿瘤，将右肾推移至左上腹象限。在剖腹手术中，肿瘤被广泛切除，右肾得以成功保留。最终组织学检查确定肿瘤为血管平滑肌脂肪瘤。术后4个月随访时，未发现肿瘤复发迹象，右肾功能完全正常。
