Tokunaga Chiho, Hiramatsu Yuji, Horigome Hitoshi, Takahashi-Igari Miho, Noma Mio, Sakakibara Yuzuru
Department of Cardiovascular Surgery, University of Tsukuba, Tsukuba 305-8575, Japan.
Ann Thorac Surg. 2003 Dec;76(6):2093-4. doi: 10.1016/s0003-4975(03)01038-5.
An infant with factor VII deficiency underwent palliative open heart surgery for pulmonary atresia with an intact ventricular septum. No references had been found on the management of this rare coagulation disorder in infantile cardiac surgery. We describe the peri- and postoperative management with a replacement therapy including a recombinant factor VIIa concentrate. We conclude that an appropriate replacement therapy is needed to control bleeding during open heart surgery with factor VII deficiency.
