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多发性硬化症中的脊髓固有肌阵挛

Propriospinal myoclonus in multiple sclerosis.

作者信息

Kapoor R, Brown P, Thompson P D, Miller D H

机构信息

University Department of Clinical Neurology, National Hospital for Neurology and Neurosurgery, London, UK.

出版信息

J Neurol Neurosurg Psychiatry. 1992 Nov;55(11):1086-8. doi: 10.1136/jnnp.55.11.1086.

DOI:10.1136/jnnp.55.11.1086
PMID:1469408
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1015299/
Abstract

The clinical and electrophysiological features of segmental myoclonus affecting the right arm and upper trunk are described in a patient with multiple sclerosis. Electrophysiological studies suggested that the myoclonus was propagated from a generator site in the cervical cord, where lesions were found using MRI. The spread of electromyographic activity in each myoclonic jerk was slow and variable. These findings are characteristic of propriospinal myoclonus, which has not been associated with multiple sclerosis previously.

摘要

一名患有多发性硬化症的患者出现了影响右臂和上躯干的节段性肌阵挛,本文描述了其临床和电生理特征。电生理研究表明,肌阵挛是从颈髓的一个起源部位传播而来的,通过磁共振成像(MRI)在该部位发现了病变。每次肌阵挛发作时肌电图活动的传播缓慢且多变。这些发现是脊髓性肌阵挛的特征,此前脊髓性肌阵挛与多发性硬化症并无关联。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2537/1015299/b3a6f2f31286/jnnpsyc00496-0106-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2537/1015299/c7dcbfd14551/jnnpsyc00496-0106-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2537/1015299/b3a6f2f31286/jnnpsyc00496-0106-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2537/1015299/c7dcbfd14551/jnnpsyc00496-0106-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2537/1015299/b3a6f2f31286/jnnpsyc00496-0106-b.jpg

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Experimental myoclonus of thalamic origin.丘脑起源的实验性肌阵挛
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Neurology. 2014 Nov 11;83(20):1862-70. doi: 10.1212/WNL.0000000000000982. Epub 2014 Oct 10.
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Philos Trans R Soc Lond B Biol Sci. 1999 Oct 29;354(1390):1649-73. doi: 10.1098/rstb.1999.0510.
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The spectrum of cortical myoclonus. From focal reflex jerks to spontaneous motor epilepsy.皮质肌阵挛的范围。从局灶性反射性抽搐到自发性运动性癫痫。
Brain. 1985 Mar;108 ( Pt 1):193-24. doi: 10.1093/brain/108.1.193.
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Segmental myoclonus. Clinical and pharmacologic study.节段性肌阵挛。临床与药理学研究。
Arch Neurol. 1986 Oct;43(10):1025-31. doi: 10.1001/archneur.1986.00520100039012.
6
Myoclonus in a patient with spinal cord transection. Possible involvement of the spinal stepping generator.一名脊髓横断患者出现肌阵挛。脊髓步进发生器可能受累。
Brain. 1988 Oct;111 ( Pt 5):1235-45. doi: 10.1093/brain/111.5.1235.
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Axial myoclonus of propriospinal origin.脊髓固有性起源的轴索性肌阵挛
Brain. 1991 Feb;114 ( Pt 1A):197-214.
8
A case of postanoxic encephalopathy with cortical action and brainstem reticular reflex myoclonus.一例伴有皮质性动作和脑干网状反射性肌阵挛的缺氧后脑病病例。
Mov Disord. 1991;6(2):139-44. doi: 10.1002/mds.870060209.
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Reticular reflex myoclonus: a physiological type of human post-hypoxic myoclonus.网状反射性肌阵挛:人类缺氧后肌阵挛的一种生理类型。
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