Raj R S, Najeeb S, Aruna R, Pavithran K, Thomas M
Medical College Hospital, Thiruvananthapuram - 695 011, India.
Indian J Cancer. 2003 Jul-Sep;40(3):116-7.
Plasma Cell Leukemia (PCL) is a rare form of plasma cell dyscrasia. Plasma cell leukemia has two variants: the primary form presents de novo in patients with no previous history of multiple myeloma (MM); the secondary form consists of a leukemic transformation in a previously recognized MM. In contrast to myeloma, PCL has an aggressive course. Median age at presentation is usually above 50 years. Here we report a case of primary PCL presenting at age of 21 years, which is extremely rare. She was treated with combination chemotherapy (VAD). Although she had a good response initially, later the disease progressed and she died 6 months after the diagnosis.
浆细胞白血病(PCL)是一种罕见的浆细胞发育异常形式。浆细胞白血病有两种变体:原发性形式在既往无多发性骨髓瘤(MM)病史的患者中初发;继发性形式由先前确诊的MM发生白血病转化而成。与骨髓瘤不同,PCL病程侵袭性强。发病时的中位年龄通常在50岁以上。在此我们报告一例21岁发病的原发性PCL病例,极为罕见。她接受了联合化疗(VAD)。尽管最初反应良好,但疾病后来进展,确诊后6个月死亡。