Rodrigues Rosana, Marchiori Edson, Müller Nestor L
Hospital Universitario Clementino Fraga Filho, Rio de Janeiro, Brazil.
J Comput Assist Tomogr. 2004 Jan-Feb;28(1):52-4. doi: 10.1097/00004728-200401000-00008.
Niemann-Pick disease is a rare inherited disorder characterized by deposition of sphingomyelin in various organs. We describe the high-resolution computed tomography findings in 2 adult sisters with Niemann-Pick disease and extensive pulmonary involvement. The main abnormalities consisted of thickening of the interlobular septa and patchy areas of ground-glass attenuation.
