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病例报告。尼曼-匹克病B型的肺部受累:CT表现。

Case report. Pulmonary involvement in Niemann-Pick disease subtype B: CT findings.

作者信息

Ferretti G R, Lantuejoul S, Brambilla E, Coulomb M

机构信息

Department of Radiology, Hôpital Michallon, CHU Grenoble, France.

出版信息

J Comput Assist Tomogr. 1996 Nov-Dec;20(6):990-2. doi: 10.1097/00004728-199611000-00023.

DOI:10.1097/00004728-199611000-00023
PMID:8933805
Abstract

We present a case of Niemann-Pick disease subtype B in which the excessive storage of sphingomyelin within lung interstitium and alveoli produced an infiltrative lung disease demonstrated on high-resolution CT (HRCT). HRCT findings were correlated to pathological features.

摘要

我们报告一例B型尼曼-匹克病,其中肺间质和肺泡内鞘磷脂过度蓄积导致了一种在高分辨率CT(HRCT)上表现为浸润性肺病的情况。HRCT表现与病理特征相关。

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