Ferretti G R, Lantuejoul S, Brambilla E, Coulomb M
Department of Radiology, Hôpital Michallon, CHU Grenoble, France.
J Comput Assist Tomogr. 1996 Nov-Dec;20(6):990-2. doi: 10.1097/00004728-199611000-00023.
We present a case of Niemann-Pick disease subtype B in which the excessive storage of sphingomyelin within lung interstitium and alveoli produced an infiltrative lung disease demonstrated on high-resolution CT (HRCT). HRCT findings were correlated to pathological features.
我们报告一例B型尼曼-匹克病,其中肺间质和肺泡内鞘磷脂过度蓄积导致了一种在高分辨率CT(HRCT)上表现为浸润性肺病的情况。HRCT表现与病理特征相关。