Nargozian Charles
Department of Anesthesiology, The Children's Hospital, Boston, MA 02115-5737, USA.
Paediatr Anaesth. 2004 Jan;14(1):53-9. doi: 10.1046/j.1460-9592.2003.01200.x.
Airway management for patients with craniofacial disorders poses many challenges. The anaesthesiologist must be familiar with the normal bony and soft-tissue anatomy in the airway and how anatomy is altered by various congenital disorders. Specific areas to assess include the oral cavity, anterior mandibular space, maxilla, temporomandibular joint and vertebral column. Congenital conditions that may alter normal anatomy and therefore anaesthetic management include cleft lip and palate with or without Pierre Robin syndrome, craniofacial dysostosis, mandibulofacial dysostosis/Treacher Collins syndrome, hemifacial microsomia, Klippel-Feil syndrome, Beckwith-Wiedemann syndrome, trisomy 21/Down's syndrome, Freeman-Sheldon/whistling face syndrome/craniocarpotarsal dysplasia, fibrodysplasia ossificans progressiva, mucopolysaccharidosis and vascular malformations.
为患有颅面疾病的患者进行气道管理面临诸多挑战。麻醉医生必须熟悉气道的正常骨骼和软组织解剖结构,以及各种先天性疾病如何改变解剖结构。需要评估的特定区域包括口腔、下颌前部间隙、上颌骨、颞下颌关节和脊柱。可能改变正常解剖结构并因此影响麻醉管理的先天性疾病包括唇腭裂伴或不伴皮埃尔·罗宾综合征、颅面骨发育不全、下颌面骨发育不全/特雷彻·柯林斯综合征、半侧颜面短小畸形、克利佩尔-费尔综合征、贝克威思-维德曼综合征、21三体综合征/唐氏综合征、弗里曼-谢尔登综合征/吹口哨面容综合征/颅腕跗骨发育不良、进行性骨化性纤维发育不良、黏多糖贮积症和血管畸形。