Teramoto Takahide, Kaneko Hideo, Funato Michinori, Sawa Hirofumi, Nagashima Kazuo, Hirose Yoshinobu, Kondo Naomi
Department of Pediatrics, Gifu University School of Medicine, 40 Tsukasa-machi, Gifu 500-8705, Japan.
Scand J Infect Dis. 2003;35(11-12):909-10. doi: 10.1080/00365540310016673.
To our knowledge, this is the first case report describing progressive multifocal leukoencephalopathy (PML) associated with X-linked agammaglobulinemia. The JC virus was confirmed at autopsy and PML was diagnosed. Humoral immunodeficiency with normal cellular immunity could be infected with JCV.
据我们所知,这是首例描述与X连锁无丙种球蛋白血症相关的进行性多灶性白质脑病(PML)的病例报告。尸检时证实了JC病毒感染并诊断为PML。具有正常细胞免疫的体液免疫缺陷可能会感染JC病毒。