部分菱形脑融合
Partial rhombencephalosynapsis.
作者信息
Demaerel Philippe, Morel Catherine, Lagae Lieven, Wilms Guido
机构信息
Department of Radiology, University Hospitals, Leuven, Belgium.
出版信息
AJNR Am J Neuroradiol. 2004 Jan;25(1):29-31.
Abstract
We describe an infant in whom partial rhombencephalosynapsis was diagnosed by using MR imaging. The anterior vermis and nodulus were normally developed, but part of the posterior vermis was deficient. There was partial fusion of the hemispheres in the inferior part of the cerebellum. Partial rhombencephalosynapsis is described for the first time, and our findings support the recent embryologic observations.
摘要
我们描述了一名通过磁共振成像诊断为部分菱形脑融合的婴儿。小脑蚓部前部和小结发育正常，但部分小脑蚓部后部缺失。小脑下部的半球存在部分融合。首次描述了部分菱形脑融合，我们的发现支持了最近的胚胎学观察结果。
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