Utsunomiya H, Takano K, Ogasawara T, Hashimoto T, Fukushima T, Okazaki M
Department of Diagnostic Radiology, Fukuoka University Hospital, Japan.
AJNR Am J Neuroradiol. 1998 Mar;19(3):547-9.
We describe two infants in whom rhombencephalosynapsis was diagnosed with MR imaging in vivo. In contrast to Dandy-Walker malformation, the vermian maldevelopment in this anomaly is characterized by an absence of the anterior vermis and a deficiency of the posterior vermis. The cerebellar hemispheres are fused. In an attempt to identify the pathogenesis of these anatomic manifestations, we question the traditional concept of the embryologic development of the cerebellar primordium.
我们描述了两名通过活体磁共振成像（MR）诊断为菱脑融合的婴儿。与丹迪-沃克畸形不同，这种异常中的蚓部发育异常的特征是前蚓部缺如和后蚓部发育不全。小脑半球融合。为了确定这些解剖学表现的发病机制，我们对小脑原基胚胎发育的传统概念提出了质疑。
