Reimund J M, Duclos B, Chamouard P, Warter J M, Weill J P, Baumann R
Service d'Hépato-Gastroentérologie et d'Assistance Nutritive, Hôpital de Hautepierre, Strasbourg, France.
Dig Dis Sci. 1992 Dec;37(12):1922-5. doi: 10.1007/BF01308090.
The occurrence of multiple carcinoid tumors of the small bowel with liver metastases is reported in a patient with a previous myotonic dystrophy. In addition to the association of myotonic dystrophy with multiple endocrine adenomatosis type 2A, hyperparathyroidism, and neurofibromatosis, this case report gives further evidence for the propensity of such patients to develop neuroendocrine tumors.
据报道，一名曾患强直性肌营养不良的患者出现了伴有肝转移的小肠多发性类癌肿瘤。除了强直性肌营养不良与2A型多发性内分泌腺瘤病、甲状旁腺功能亢进和神经纤维瘤病有关外，本病例报告进一步证明了这类患者发生神经内分泌肿瘤的倾向。
