[阿拉吉列综合征与慢性肾衰竭]
[Alagille syndrome and chronic renal failure].
作者信息
Kaczyńska Anna, Lewandowski Jacek, Pruszczyk Piotr, Gaciong Zbigniew
机构信息
Katedra i Klinika Chorób Wewnetrznych i Nadciśnienia Tetniczego AM w Warszawie.
出版信息
Pol Arch Med Wewn. 2003 May;109(5):511-5.
PMID:14768181
Abstract
Alagille syndrome is characterized by paucity of bile ducts leading to cholestasis and may be accompanied by renal and cardiovascular abnormalities. We report 42-years old patient with hypertension, chronic renal failure and Alagille syndrome. Ischemic nephropathy was suspected, which was not confirmed on angio-CT. It seems, that chronic renal failure in the patient was due to primary parenchymal pathology.
摘要
阿拉吉列综合征的特征是胆管缺乏导致胆汁淤积，可能伴有肾脏和心血管异常。我们报告了一名42岁患有高血压、慢性肾衰竭和阿拉吉列综合征的患者。怀疑为缺血性肾病，但血管CT未证实。该患者的慢性肾衰竭似乎是由于原发性实质病变。
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