儿童原发性空蝶鞍综合征与尿崩症

The primary empty-sella syndrome and diabetes insipidus in a child.

作者信息

Hung W, Fitz C R

机构信息

Department of Endocrinology and Metabolism, Children's National Medical Center, Washington, DC.

出版信息

Acta Paediatr. 1992 May;81(5):459-61. doi: 10.1111/j.1651-2227.1992.tb12273.x.

DOI:10.1111/j.1651-2227.1992.tb12273.x

PMID:1498518

Abstract

The empty-sella syndrome is uncommon in pediatric patients. Hypothalamic-pituitary dysfunction is common in these patients but involvement of the posterior pituitary gland is very rare. We report a seven-year-old girl with empty-sella syndrome who first developed arginine-vasopressin deficient diabetes insipidus and then anterior pituitary gland deficiency. The empty-sella syndrome should be included among the causes of arginine-vasopressin deficient diabetes insipidus in pediatric patients.

摘要

空蝶鞍综合征在儿科患者中并不常见。下丘脑-垂体功能障碍在这些患者中很常见，但垂体后叶受累非常罕见。我们报告了一名七岁患有空蝶鞍综合征的女孩，她首先出现精氨酸加压素缺乏性尿崩症，随后出现垂体前叶功能减退。空蝶鞍综合征应被列入儿科患者精氨酸加压素缺乏性尿崩症的病因之中。