Azoulay Robin, Brisse Hervé, Fréneaux Paul, Ferey Solène, Kalifa Gabriel, Adamsbaum Catherine
Department of Pediatric Radiology, Hôpital St-Vincent-de Paul, Institut Curie, 82 Avenue Denfert-Rochereau, 75674 Paris, France.
AJNR Am J Neuroradiol. 2004 Mar;25(3):498-500.
A 7-year-old West African male patient presented with recurrence of multiple cervical lymphadenopathy. Cervical node biopsy disclosed a sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman-Destombes disease). During follow-up, the patient developed a left orbital mass corresponding to an enlarged lacrimal gland shown by CT. The histologic features of the gland were consistent with the diagnosis, and with steroid treatment, the gland decreased in size. Although rare, the diagnosis of sinus histiocytosis with massive lymphadenopathy has to be considered in cases of lacrimal gland enlargement.
一名7岁西非男性患者出现多发性颈部淋巴结病复发。颈部淋巴结活检显示为伴有巨大淋巴结病的窦组织细胞增生症(罗萨伊-多夫曼-德斯顿贝斯病)。在随访期间,患者出现左侧眼眶肿物,CT显示为泪腺肿大。泪腺的组织学特征与诊断相符,经类固醇治疗后,泪腺体积缩小。尽管罕见,但在泪腺肿大的病例中必须考虑伴有巨大淋巴结病的窦组织细胞增生症的诊断。