Vormoor J, Ritter J, Creutzig U, Boos J, Heyen P, Ludwig W D, Harbott J, Löffler H, Schellong G
Department of Paediatric Haematology and Oncology, University of Münster, Germany.
Br J Cancer Suppl. 1992 Aug;18:S63-7.
Clinical, morphological, immunological, cytogenetical and prognostic features of 84 children under 2 years of age with AML in studies AML-BFM-78, -83 and -87 were retrospectively analysed. There was a high incidence of acute monoblastic leukaemia (FAB M5) (41 patients--49%) and acute megakaryoblastic leukaemia (FAB M7) (study AML-BFM-87: five patients--13%) in this age group. Acute monoblastic leukaemia was associated with hepatosplenomegaly, extramedullary organ manifestations and chromosomal abnormalities involving 11q23. The probability of an 11-year event-free survival of all patients under 2 years of the three studies combined was 39% (SD 6%). While the event-free survival rates of patients aged 2 years and older could be improved in studies AML-BFM-83 and -87 compared with study AML-BFM-78, overall prognosis in children under 2 years in the three consecutive studies remained unchanged. The event-free survival rate of children with acute monoblastic leukaemia in both age groups was comparable (7 yr-EFS (AML-BFM-83 and -87): much less than 2 years--43% (SD 9%), =/much greater than 2 years--33% (SD 9%); P much greater than 0.5). This also applied to other risk groups. In conclusion, taking the high incidence of acute monoblastic and megakaryoblastic leukaemia in children under 2 years into account, no significant differences between children under 2 years or older children concerning response to therapy and overall prognosis could be evaluated.
对AML-BFM-78、-83和-87研究中84例2岁以下急性髓系白血病(AML)患儿的临床、形态学、免疫学、细胞遗传学和预后特征进行了回顾性分析。该年龄组急性单核细胞白血病(FAB M5)(41例,占49%)和急性巨核细胞白血病(FAB M7)(AML-BFM-87研究:5例,占13%)的发病率较高。急性单核细胞白血病与肝脾肿大、髓外器官表现以及涉及11q23的染色体异常有关。三项研究中所有2岁以下患儿11年无事件生存率为39%(标准差6%)。与AML-BFM-78研究相比,AML-BFM-83和-87研究中2岁及以上患儿的无事件生存率有所提高,但三项连续研究中2岁以下患儿的总体预后保持不变。两个年龄组急性单核细胞白血病患儿的无事件生存率相当(7年无事件生存率(AML-BFM-83和-87):小于2岁组为43%(标准差9%),大于2岁组为33%(标准差9%);P大于0.5)。其他风险组也是如此。总之,考虑到2岁以下儿童急性单核细胞白血病和急性巨核细胞白血病的高发病率,无法评估2岁以下儿童与2岁及以上儿童在治疗反应和总体预后方面的显著差异。