Calugaru M, Barsu M
Department of Ophthalmology, Medical School, University of Cluj-Napoca, Romania.
Graefes Arch Clin Exp Ophthalmol. 1992;230(4):352-7. doi: 10.1007/BF00165944.
The clinical and histopathological findings are described in a 10-year-old girl with xeroderma pigmentosum and multiple ophthalmic complications, including the eyelids, conjunctiva, orbit, cornea and iris; some of these complications took an unusual form. Histological examination following right orbital exenteration revealed an epibulbar squamous cell carcinoma penetrating the orbit and building a noose all around the ocular globe with subsequent strangulation. Moreover, a palpebral squamous cell carcinoma developed independently from the right lower lid and, unconnected with the epibulbar tumor, penetrated to the orbit.
本文描述了一名患有色素性干皮病并伴有多种眼部并发症（包括眼睑、结膜、眼眶、角膜和虹膜）的10岁女孩的临床和组织病理学发现；其中一些并发症表现出不寻常的形式。右眼眶内容剜除术后的组织学检查显示，眼球表面鳞状细胞癌侵犯眼眶并在眼球周围形成套索，继而导致绞窄。此外，睑部鳞状细胞癌独立发生于右下眼睑，与眼球表面肿瘤无关，且侵犯至眼眶。
