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无症状性Brugada综合征与体位性直立性心动过速综合征相关:自主神经功能紊乱是否会增加未来心律失常事件的发生倾向?

Asymptomatic Brugada syndrome associated with postural orthostatic tachycardia syndrome: Does autonomic disorder increase propensity for future arrhythmic events?

作者信息

Morishima Itsuro, Sone Takahito, Tsuboi Hideyuki, Mukawa Hiroaki, Satoda Masahiko, Uesugi Michitaka

机构信息

Department of Cardiology, Ogaki Municipal Hospital, Ogaki, Japan.

出版信息

Pacing Clin Electrophysiol. 2004 Apr;27(4):537-40. doi: 10.1111/j.1540-8159.2004.00477.x.

DOI:10.1111/j.1540-8159.2004.00477.x
PMID:15078411
Abstract

Autonomic imbalance may work as a modifying factor for initiating lethal arrhythmia in patients with Brugada syndrome. A 26-year-old man with episodes of near syncope was given a diagnosis of an autonomic disorder, postural orthostatic tachycardia syndrome (POTS). The patient spontaneously showed typical Brugada-type ECG, and ventricular fibrillation was induced by programmed electrical stimulation, which allowed the further diagnosis of Brugada syndrome. Although it seems that Brugada syndrome is asymptomatic, its uncommon association of POTS may increase the risk for future arrhythmic events in this patient.

摘要

自主神经失衡可能是引发Brugada综合征患者致命性心律失常的一个修饰因素。一名26岁有接近晕厥发作的男性被诊断为自主神经功能障碍,即体位性直立性心动过速综合征(POTS)。该患者自发出现典型的Brugada型心电图,经程序电刺激诱发室颤,从而进一步确诊为Brugada综合征。尽管Brugada综合征看似无症状,但其与POTS的罕见关联可能会增加该患者未来发生心律失常事件的风险。

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