Majorana A, Facchetti F
Clinica Odontoiatrica, Università di Brescia.
Minerva Stomatol. 1992 Mar;41(3):127-33.
Ehlers-Danlos syndrome (EDs) is a hereditary disorder of the connective tissue. Its clinical expression is variable and there are many difficulties in recognizing the disease because of the presence of eleven different forms. In this study the authors describe the oral manifestations in two cases of EDs. The children show hyperelasticity of the skin, easy bruisability, hyperextensibility of the joints, several dental manifestations: periodontitis, many caries, supernumerary teeth or hypodontia.
埃勒斯-当洛综合征（EDS）是一种遗传性结缔组织疾病。其临床表现多样，由于存在11种不同形式，该病的识别存在诸多困难。在本研究中，作者描述了两例EDS患者的口腔表现。这些患儿表现出皮肤弹性过度、易瘀斑、关节伸展过度，以及多种牙齿表现：牙周炎、多发龋齿、多生牙或牙齿发育不全。
