Akassoglou Katerina, Adams Ryan A, Bauer Jan, Mercado Peter, Tseveleki Vivian, Lassmann Hans, Probert Lesley, Strickland Sidney
Department of Pharmacology, University of California at San Diego, La Jolla, CA 92093-0636, USA.
Proc Natl Acad Sci U S A. 2004 Apr 27;101(17):6698-703. doi: 10.1073/pnas.0303859101. Epub 2004 Apr 19.
In multiple sclerosis, in which brain tissue becomes permeable to blood proteins, extravascular fibrin deposition correlates with sites of inflammatory demyelination and axonal damage. To examine the role of fibrin in neuroinflammatory demyelination, we depleted fibrin in two tumor necrosis factor transgenic mouse models of multiple sclerosis, transgenic lines TgK21 and Tg6074. In a genetic analysis, we crossed TgK21 mice into a fibrin-deficient background. TgK21fib(-/-) mice had decreased inflammation and expression of major histocompatibility complex class I antigens, reduced demyelination, and a lengthened lifespan compared with TgK21 mice. In a pharmacologic analysis, fibrin depletion, by using the snake venom ancrod, in Tg6074 mice also delayed the onset of inflammatory demyelination. Overall, these results indicate that fibrin regulates the inflammatory response in neuroinflammatory diseases. Design of therapeutic strategies based on fibrin depletion could potentially benefit the clinical course of demyelinating diseases such as multiple sclerosis.
在多发性硬化症中,脑组织会对血液中的蛋白质变得通透,血管外纤维蛋白沉积与炎性脱髓鞘和轴突损伤部位相关。为了研究纤维蛋白在神经炎性脱髓鞘中的作用,我们在两种多发性硬化症的肿瘤坏死因子转基因小鼠模型(转基因系TgK21和Tg6074)中消耗了纤维蛋白。在一项基因分析中,我们将TgK21小鼠与纤维蛋白缺陷背景进行杂交。与TgK21小鼠相比,TgK21fib(-/-)小鼠的炎症和主要组织相容性复合体I类抗原的表达减少,脱髓鞘减轻,寿命延长。在一项药理学分析中,使用蛇毒安克洛消耗Tg6074小鼠体内的纤维蛋白也延迟了炎性脱髓鞘的发作。总体而言,这些结果表明纤维蛋白调节神经炎性疾病中的炎症反应。基于纤维蛋白消耗设计治疗策略可能会对诸如多发性硬化症等脱髓鞘疾病的临床病程有益。