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亚急性硬化性全脑炎中肌阵挛和周期性同步放电的起源。

The origin of myoclonus and periodic synchronous discharges in subacute sclerosing panencephalitis.

作者信息

Yagi S, Miura Y, Kataoka N, Mizuta S, Wakunami A, Morita T

机构信息

Department of Pediatrics, Kawasaki Medical School, Okayama, Japan.

出版信息

Acta Paediatr Jpn. 1992 Jun;34(3):310-5. doi: 10.1111/j.1442-200x.1992.tb00964.x.

DOI:10.1111/j.1442-200x.1992.tb00964.x
PMID:1509877
Abstract

We report here a case of a patient with subacute sclerosing panencephalitis (SSPE) and we have analyzed periodic events using dipole tracing methods to clarify the origin of periodic synchronous discharges and myoclonus. Both source generators were located in the subcortical part of the cerebrum, an area adjacent to the thalamus. Although the pathophysiology of periodic events in SSPE has been controversial, dipole tracing methods may contribute to clarify the origin of periodic events in SSPE.

摘要

我们在此报告一例亚急性硬化性全脑炎(SSPE)患者,并使用偶极子追踪方法分析了周期性事件,以阐明周期性同步放电和肌阵挛的起源。两个源发生器均位于大脑皮质下部分,即与丘脑相邻的区域。尽管SSPE中周期性事件的病理生理学一直存在争议,但偶极子追踪方法可能有助于阐明SSPE中周期性事件的起源。

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Acta Paediatr Jpn. 1992 Jun;34(3):310-5. doi: 10.1111/j.1442-200x.1992.tb00964.x.
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Movement Disorders in Patients with Subacute Sclerosing Panencephalitis: A Systematic Review.亚急性硬化性全脑炎患者的运动障碍:系统评价。
Mov Disord Clin Pract. 2024 Jul;11(7):770-785. doi: 10.1002/mdc3.14062. Epub 2024 May 15.
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Jaw Opening Myoclonus in Subacute Sclerosing Panencephalitis.亚急性硬化性全脑炎中的张口肌阵挛
Mov Disord Clin Pract. 2023 Aug 24;10(Suppl 3):S63-S65. doi: 10.1002/mdc3.13782. eCollection 2023 Aug.
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Fulminant adult-onset subacute sclerosing panencephalitis: a case report.暴发性成人起病亚急性硬化性全脑炎:一例报告
BMJ Case Rep. 2009;2009. doi: 10.1136/bcr.09.2008.0922. Epub 2009 Mar 2.