Gómez-Oliveira Guillermo, Fernández-Alba Luengo Javier, Martín-Sastre Roberto, Patiño-Seijas Beatriz, López-Cedrún-Cembranos José Luis
Servicio de Cirugía Macilofacial, CHU Juan Canalejo, La Coruña, Spain.
Med Oral. 2004 May-Jul;9(3):263-7.
The case reported deals with a solitary plexiform neurofibroma affecting the cheek submucosa. Neurofibroma is an uncommon tumor which rarely appears in oral cavity but it represents the most common neurogenic tumor. Furthermore, plexiform variety is less frequent. Clinically, oral neurofibromas usually appears as anodyne and asintomatic lesions. Sometimes, they produce nervous compression. In this case, tumor is big but asintomatic. There is no definitive radiologic image. It has association with polyglandular syndromes and phacomatosis. The treatment of choice is excision. There are doubts of the surgical results so that some authors are looking for new non-surgical treatments. The clinical characteristics, epidemiology, diagnosis and treatment are described as soon as a bibliographic revisión.
所报道的病例为一例累及颊黏膜下层的孤立性丛状神经纤维瘤。神经纤维瘤是一种罕见的肿瘤,很少出现在口腔,但它是最常见的神经源性肿瘤。此外,丛状型更为少见。临床上,口腔神经纤维瘤通常表现为无痛性、无症状性病变。有时,它们会引起神经受压。在本病例中,肿瘤较大但无症状。没有明确的影像学表现。它与多腺体综合征和错构瘤有关。首选的治疗方法是切除。对手术结果存在疑问,因此一些作者正在寻找新的非手术治疗方法。通过文献复习对其临床特征、流行病学、诊断和治疗进行了描述。