Yigit Taner, Yigitler Cengizhan, Gulec Bulent, Ozcan Ayhan, Kozak Orhan, Mesut Pekcan
Departement de Chirurgie Générale, Gulhane Military Medical Academy, Ankara, Turquie.
Prog Urol. 2004 Apr;14(2):207-9.
Renal Angiomyolipoma (AML) is a rare benign tumor As it is usually asymptomatic and small, AML sometimes may cause acute abdomen by spontaneous rupture and hemorrhage that may be life threatening in some cases for which surgical management is necessary. A 58-year-old female patient was admitted for right side and right upper abdominal pain, nausea and vomiting. Right upper abdominal and right side sensitivity were remarkable on physical examination. Whole blood count revealed the ongoing with steady remarkable decrement in hematocrite and hemoglobin. Radiological examination showed right kidney mass with retroperitoneal hematoma. Patient underwent a right nephrectomy with mass excision. Her postoperative period was uneventful. On this case report we conclude that; angiomyolipoma may cause serious complications by the spontaneous rupture and life threatening hemorrhage. In case of massive hemorrhage and/or whole renal involvement, nephrectomy is the most feasible surgical treatment of all the other treatment methods.
肾血管平滑肌脂肪瘤（AML）是一种罕见的良性肿瘤。由于它通常无症状且体积较小，AML有时可能会因自发破裂和出血而导致急腹症，在某些情况下可能危及生命，因此需要进行手术治疗。一名58岁女性患者因右侧及右上腹疼痛、恶心和呕吐入院。体格检查发现右上腹和右侧有明显压痛。全血细胞计数显示血细胞比容和血红蛋白持续稳步显著下降。影像学检查显示右肾肿块伴腹膜后血肿。患者接受了右肾切除术及肿块切除术。术后恢复顺利。在本病例报告中我们得出结论：血管平滑肌脂肪瘤可能因自发破裂和危及生命的出血而导致严重并发症。在发生大出血和/或整个肾脏受累的情况下，肾切除术是所有其他治疗方法中最可行的手术治疗方式。
